A carotid body tumor is a tumor of neurovascular origin arising from the chemoreceptor cells in the carotid sheath, most commonly located at the bifurcation of the carotid artery. The majority of the blood supply of the tumor comes from the peripheral branches of the external carotid artery. Shamblin classified carotid body tumors into three categories, based on the relationship of the carotid arteries and the adjoining nerves to the tumor. In type I tumors, the arteries are simply displaced by the tumor and lie on the surface of the tumor. In type II, the tumor is indented by the external and internal carotid arteries, making a deep groove within the tumor and the hypoglossal and superior laryngeal nerves are on the tumor's surface. In type III the arteries and the nerves are encased by the tumor. MRI imaging is required to demonstrate the location and extent of these tumors as well as the relationship of carotid vessels to the tumor. An MR angiogram or digital intravenous angiography provides information to plan the indicated surgery. Selection of treatment depends on the size and location of the tumor, the surgical risk, and the risk of cranial nerve deficits resulting from surgery versus the potential benefit to be derived from non-surgical treatment. We present a case of a patient with a right sided carotid body tumor. The patient presented with a pulsatile mass on the right upper neck and examination of the oropharynx showed deviation of the lateral pharyngeal wall medially by the mass. T1 weighted MRI axial views with gadolinium contrast enhancement demonstrate a tumor mass separating the internal and external carotid arteries. The arteries are partially embedded within the substance of the tumor typical of a Shamblin type II tumor. An MR angiogram demonstrates splaying of the external and internal carotid artery. In this patient the tumor was small and unifocal and therefore surgical excision was recommended to prevent progressive neurologic deficit due to an enlarging tumor mass. The operative procedure for this uncommon operation is described in detail in the video.